We report a rare case of a 73-year-old man who was presented with an 8-year history of progressive pruritic skin discoloration. Homogeneous dark brown to black hyperpigmentation involving the face, neck, axillae extensor surfaces of the extremities, back, abdomen, and the gluteal regions were noted. No popular or rippled skin lesions were observed. The skin biopsy revealed amyloid deposits in papillary dermis. Detailed clinical and laboratory examinations showed no evidence of any systemic amyloidosis. The patient was diagnosed with primary diffuse macular cutaneous amyloidosis, which is an unusual skin disorder. In this report, besides discussing the present case, the pathogenesis and clinical and histopathological features of macular cutaneous amyloidosis are reviewed as well.