Hereditary hemorrhagic telangiectasia (HHT) is a rare autosomal dominant inherited disorder. Typical finding of the disease telangiectasias in skin and mucous membranes, and arteriovenous malformations and aneurysyms that occur in the organs like brain, lung, intestine and liver. A wide variety of clinical manifestations in HHT have been described. Most of the patients are epistaxis in the application, then telangiectasias and visceral organ involvements occur. Here we report a case having typical skin lesions among with visceral organ findings, and that was diagnosed as HHT.